A unique approach to Fontan revision in a cyanotic patient
Prog Pediatr Cardiol
© 2020 Elsevier B.V. Unilateral pulmonary arteriovenous malformations can develop in heterotaxy patients with single ventricle physiology after Kawashima procedure due to preferential flow streaming to one lung. We present the case of a 25 year old patient with this physiology who presented with resting cyanosis to 75% in room air. Our patient underwent a unique revision to reverse the development of arteriovenous malformations with partial resection of her hepatic vein-right pulmonary artery conduit and placement of new conduit connecting hepatic veins to innominate vein which then drained into left-sided superior vena cava, resulting in favorable outcome.
School of Medicine
Cardiovascular and Thoracic Surgery