Supratentorial Neurenteric Cysts: Case Series and Review of Pathology, Imaging, and Clinical Management
BACKGROUND: Neurenteric cysts are rare congenital lesions along the neuroaxis, typically found in the spine, and rarely intracranially. Here, we present three patients who presented to our institution over a six year period with supratentorial intracranial neurenteric cysts and conduct a comprehensive review of the literature to describe the salient pathology, radiological features, and clinical issues regarding these lesions. CASES: Three patients were treated surgically for supratentorial neurenteric cysts. One patient presented in extremis, while the others were treated electively. Each patient presented with significantly different signs and symptoms, and unique radiological findings. All patients were neurologically intact after surgery. CONCLUSIONS: Neurenteric cysts present with a variety of signs and symptoms. Given the increased use of neuroimaging, supratentorial neurenteric cysts may be encountered more frequently; and are important to include on the differential diagnosis and managed accordingly. Post-operative seizures occur in over 20%, even in patients who had no pre-operative seizures. Surgical treatment can be done safely with good neurological outcomes.
Faculty, Northwell Researcher
School of Medicine; Northwell Health