Publication Date
2015
Journal Title
Case Rep Hematol
Abstract
Spontaneous (nontraumatic) acute epidural hematoma is a rare and poorly understood complication of sickle cell disease. A 19-year-old African American male with hemoglobin SC disease (HbSC) presented with generalized body aches and was managed for acute painful crisis. During his hospital stay he developed rapid deterioration of his mental status and computed topography revealed a spontaneous massive epidural hematoma with mass effect and midline shift with Kernohan's notch phenomena for which urgent craniotomy and evacuation was done. We report the first case of HbSC disease associated with catastrophic epidural hematoma progressing to transtentorial herniation and Kernohan's notch phenomena within few hours with rapid clinical deterioration. The etiopathogenesis and the rare presentation are discussed in detail in this case report.
Volume Number
2015
Pages
470873
Document Type
Article
EPub Date
2015/11/18
Status
Faculty
Facility
School of Medicine
Primary Department
Neurosurgery
PMID
DOI
10.1155/2015/470873