A rare case of double-chambered right ventricle associated with ventricular septal defect and congenital absence of the pulmonary valve

Authors

G. Khoueiry, Northwell Health
T. Bhat, Northwell Health
M. Tantray, Northwell Health
M. Meghani, Northwell Health
N. Abi Rafeh, Northwell Health
M. Abdallah, Northwell Health
W. Hoyek, Northwell Health

Publication Date

2014

Journal Title

Clin Med Insights Circ Respir Pulm Med

Abstract

Double-chambered right ventricle (DCRV) is a rare congenital heart disorder involving 2 different right ventricle (RV) pressure compartments that is often associated with ventricular septal defect (VSD). Usually, the obstruction is caused by an anomalous muscle bundle crossing the RV from the interventricular septum to the RV free wall. We are reporting a case of double-chambered right ventricle associated with ventricular septal defect and congenital absence of the pulmonary valve, a rare form of congenital infundibular pulmonary stenosis. In addition to ventricular septal defect, our patient had congenital absence of the pulmonary valve, which is very unusual and has never been reported to our knowledge.

Volume Number

8

Pages

1-3

Document Type

Article

EPub Date

2014/04/01

Status

Northwell Researcher

Facility

Northwell Health

Primary Department

General Internal Medicine

Additional Departments

Cardiology

PMID

24683307

DOI

10.4137/ccrpm.s11174