Sudden cardiac death in isolated right ventricular hypertrabeculation/noncompaction cardiomyopathy

Publication Date

2018

Journal Title

Ann Noninvasive Electrocardiol

Abstract

© 2017 Wiley Periodicals, Inc. Hypertrabeculation/noncompaction of the myocardium is a rare disorder that involves most commonly the left ventricle of the heart and it has been recognized as a distinct cardiomyopathy by the World Health Organization. However, it is extremely rare for this condition to involve exclusively the right ventricle. We report the cases of three patients who presented with ventricular tachyarrhythmia and sudden cardiac death. They were found to have isolated right ventricular hypertrabeculation/noncompaction on echocardiography. This supports the hypothesis that this condition is highly arrhythmogenic and is associated with high mortality similarly to the left ventricular hypertrabeculation/noncompaction cardiomyopathy.

Volume Number

23

Issue Number

4

Pages

e12487

Document Type

Article

Status

Faculty, Northwell Researcher, Northwell Resident

Facility

School of Medicine; Northwell Health

Primary Department

General Internal Medicine

Additional Departments

Cardiology

PMID

28901675

DOI

10.1111/anec.12487

For the public and Northwell Health campuses

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