A unique approach to Fontan revision in a cyanotic patient
Publication Date
2020
Journal Title
Prog Pediatr Cardiol
Abstract
© 2020 Elsevier B.V. Unilateral pulmonary arteriovenous malformations can develop in heterotaxy patients with single ventricle physiology after Kawashima procedure due to preferential flow streaming to one lung. We present the case of a 25 year old patient with this physiology who presented with resting cyanosis to 75% in room air. Our patient underwent a unique revision to reverse the development of arteriovenous malformations with partial resection of her hepatic vein-right pulmonary artery conduit and placement of new conduit connecting hepatic veins to innominate vein which then drained into left-sided superior vena cava, resulting in favorable outcome.
Volume Number
59
Pages
101298
Document Type
Article
Status
Faculty
Facility
School of Medicine
Primary Department
General Pediatrics
Additional Departments
Cardiovascular and Thoracic Surgery
DOI
10.1016/j.ppedcard.2020.101298